Abstract
Background:
Paget’s disease is an osteodystrophy characterized by anarchic remodeling. The combination of neurosensory and neurological complications is an exceptional disease’s discovery circumstance.
The objective is to study different aspects of this complicated form.
Here a case revealed by deafness which was combined with multiple neurological and neurosensory complications.
Observation:
A 43-year-old man complained of hypoacusis evolving for three years, combined to tinnitus, headaches, vertigo and scalp dysesthesia. Examination revealed an increased head circumference and prominent frontal bosses. Examination showed a normal otoscopy, multidirectional nystagmus, a right pyramidal syndrome and a static cerebellar syndrome. Radio-biological examination was in favour of Paget’s disease. During his exploration, the patient had developed axonal optic neuropathy. He had biphosphonates treatment. The evolution was favorable with a follow-up of 24 months.
Conclusion:
Combined neurosensory and neurological complications is an exceptional and serious situation of Paget’s disease revelation.
Key-words:
Paget’s disease – Optic Neuropathy- Sensoryneural Deafness
