Introduction: Adenoid cystic carcinoma (ACC) rarely develops in the nasopharynx. Compared with other nasopharyngeal tumors, it is characterized by a slow progression, a local aggressivity and a high tendency to recurrence.
Case presentation: We report the case of a 71-year-old patient diagnosed with locally advanced ACC of the nasopharynx treated by concomitant radio-chemotherapy.
Conclusion: Clear consensus is not available for the most appropriate management strategy for nasopharyngeal ACC.
Key words: Adenoid cystic carcinoma; Nasopharynx; Radiotherapy; Chemotherapy