Objective: Endolymphatic sac tumor (Heffner tumor/ELST) is benign, indolent but invasive arising in the posterior petrous ridge. ELST could occur sporadically or as a part of von Hippel–Lindau (VHL) disease. Morphologically, these tumors showed a papillary and glandular architecture. We report a case of endolymphatic sac tumor to discuss the diagnostic and therapeutic features of this rare entity.
Observation: A 58-year-old woman presented with one year history of slowly progressing unilateral hearing loss, tinnitus and vertigo. The patient was diagnosed with an endolymphatic sac tumor and was managed with a radiation therapy.
Conclusion: Endolymphatic sac tumor (ELST) is a rare low-grade adenocarcinoma of the skull base. Diagnosis is based on clinical, radiological, and pathological correlation and the optimal treatment is surgical resection with security respected margins. Radiotherapy remains controversial. A long term follow up is recommended.
Key-words: Endolymphatic sac tumor; Papillary tumor; Von Hippel-Lindau disease.
Actualités:
- FUNCTIONAL RESULTS OF VELAR RADIOFREQUENCY SNORING TREATMENT
- PRISE EN CHARGE DES PARALYSIES RECURRENTIELLES EN ADDUCTION : A PROPOS DE 92 CAS
- LES LESIONS BENIGNES NON TUMORALES DU LARYNX : RESULTATS THERAPEUTIQUES ET FACTEURS INFLUENÇANT
- ROLE OF USING FINE NEEDLE ASPIRATION CYTOLOGY AND FROZEN SECTION EXAMINATION IN THE DIAGNOSIS AND MANAGEMENT OF THYROID NODULES
- UNUSUAL DIAGNOSIS OF RECURRENT UNILATERAL FACIAL CELLULITIS
- PAGET’S DISEASE REVEALED BY MULTIPLE NEUROSENSORY COMPLICATIONS: A CASE REPORT
- MANAGEMENT AND CLINICAL FEATURES OF EXTRA NODAL ENT TUBERCULOSIS: ABOUT 7 CASES
- GESTION D’UNE UNITE COVID-19 AU SEIN D’UN SERVICE D’ORL ET SA REPERCUSSION SUR L’ACTIVITE ORDINAIRE : EXPERIENCE DU SERVICE D’ORL DE L’HOPITAL HABIB THAMEUR
